Explore a catalyst in IgAN disease pathogenesis
APRIL is a sustaining factor in IgAN pathogenesis through its role in Gd-IgA1 production1,2
APRIL—a cytokine, member of the TNF superfamily, and B-cell growth factor—plays a key role in5:
B-cell activation
Mucosal IgA production
The survival of long-lived plasma cells
Ig isotype class-switching
The proliferated Gd-IgA1 leads to autoantibody production, immune complex formation, inflammation, and kidney injury.5
Learn more about the impact of IgAN
APRIL=A PRoliferation-Inducing Ligand; Gd-IgA1=galactose-deficient immunoglobulin A1; Ig=immunoglobulin; IgA=immunoglobulin A; IgAN=immunoglobulin A nephropathy; TNF=tumor necrosis factor.
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References: 1.
Suzuki H, Kiryluk K, Novak J, et al. The pathophysiology of IgA nephropathy. J Am Soc Nephrol. 2011;22(10):1795-1803.
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Gutiérrez E, Carvaca-Fontán F, Luzardo L, Morales E, Alonso M, Praga M. A personalized update on IgA nephropathy: a new vision and new future challenges. Nephron. 2020;144(11):555-571.
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Cheung CK, Barratt J, Lafayette R, et al. Targeting APRIL in the treatment of glomerular diseases. Kidney Int. 2024. doi:10.1016/j.kint.2024.08.012.
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Pitcher D, Braddon F, Hendry B, et al. Long-term outcomes in IgA nephropathy. Clin J Am Soc Nephrol. 2023;18(6):727-738.
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Cheung CK, Barratt J, Liew A, Zhang H, Tesař V, Lafayette R. The role of BAFF and APRIL in lgA nephrology: pathogenic mechanisms and targeted therapies. Front Nephrol. 2024;3:1346769.
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Caster DJ, Abner CW, Walker PD, et al. Clinicopathological characteristics of adult IgA nephropathy in the United States. Kidney Int Rep. 2023;8(9):1792-1800.
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Lai KN, Tang SC, Schena FP, et al. IgA nephropathy. Nat Rev Dis Primers. 2016;2:16001.
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Cattran DC, Floege J, Coppo R. Evaluating progression risk in patients with immunoglobulin A nephropathy. Kidney Int Rep. 2023;8(12):2515-2528.
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Donadio JV, Bergstralh EJ, Grande JP, Rademcher DM. Proteinuria patterns and their association with subsequent end-stage renal disease in IgA nephropathy. Nephrol Dial Transplant. 2002;17(7):1197-1203.
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Reich HN, Troyanov S, Scholey JW, Cattran DC; Toronto Glomerulonephritis Registry. Remission of proteinuria improves prognosis in IgA nephropathy. J Am Soc Nephrol. 2007;18(12):3177-3183.
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12.
Coppo R, D’Arrigo G, Tripepi G, et al. Is there long-term value of pathology scoring in immunoglobulin A nephropathy? A validation study of the Oxford Classification for IgA Nephropathy (VALIGA) update. Nephrol Dial Transplant. 2020;35(6):1002-1009.